Autologous stem cell transplantation for paediatric-onset polyarteritis nodosa: changes in autoimmune phenotype in the context of reduced diversity of the T- and B-cell repertoires, and evidence for reversion from the CD45RO(+) to RA(+) phenotype

Rheumatology (Oxford). 2001 Nov;40(11):1299-307. doi: 10.1093/rheumatology/40.11.1299.

Abstract

We have studied immune reconstitution in a patient with paediatric-onset polyarteritis nodosa treated with high-dose immunosuppressive agents followed by stem cell rescue. The patient developed several new autoimmune phenomena over the 18 months after immunosuppression and stem cell rescue. Flow cytometry, reverse transcription-polymerase chain reaction (RT-PCR) heteroduplex and isotype-specific RT-PCR analysis of immunoglobulin expression showed that the T- and B-cell repertoires were highly restricted in the first few months after treatment. The dominant T-cell clones seen after reconstitution were persistently expanded, were different from those which could be demonstrated before autologous stem cell transplantation, and were in the CD8(+) population. Our data also show that 12 months after treatment these expanded T-cell clones were within the CD45RA(+) population, suggesting that reversion from the CD45RO(+) to the CD45RA(+) phenotype had occurred in vivo.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Age of Onset
  • B-Lymphocytes / chemistry
  • B-Lymphocytes / immunology*
  • Biomarkers
  • Female
  • Flow Cytometry
  • Gene Expression / immunology
  • Hematopoietic Stem Cell Transplantation*
  • Heteroduplex Analysis
  • Humans
  • Immunologic Memory / immunology
  • Immunosuppression Therapy
  • Leukocyte Common Antigens / analysis
  • Leukocyte Common Antigens / genetics*
  • Leukocyte Common Antigens / immunology
  • Phenotype
  • Polyarteritis Nodosa / genetics
  • Polyarteritis Nodosa / immunology*
  • Polyarteritis Nodosa / therapy*
  • T-Lymphocytes / chemistry
  • T-Lymphocytes / immunology*
  • Transplantation, Autologous

Substances

  • Biomarkers
  • Leukocyte Common Antigens