Abstract
Chronic myelogenous leukemia (CML) is a clonal hematopoetic stem cell disorder characterized by the Philadelphia chromosome and resultant production of the constitutively activated Bcr-Abl tyrosine kinase. Characterized clinically by marked myeloid proliferation, it invariably terminates in an acute leukemia. Conventional therapeutic options include interferon-based regimens and stem cell transplantation, with stem cell transplantation being the only curative therapy. Through rational drug development, STI571, a Bcr-Abl tyrosine kinase inhibitor, has emerged as a paradigm for gene product targeted therapy, offering new hope for expanded treatment options for patients with CML.
MeSH terms
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Antineoplastic Agents / therapeutic use
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Benzamides
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Enzyme Activation
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Fusion Proteins, bcr-abl
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Hematopoietic Stem Cell Transplantation
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Humans
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Imatinib Mesylate
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Interferons / therapeutic use
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Leukemia, Myelogenous, Chronic, BCR-ABL Positive / diagnosis
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Leukemia, Myelogenous, Chronic, BCR-ABL Positive / genetics
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Leukemia, Myelogenous, Chronic, BCR-ABL Positive / therapy*
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Piperazines / therapeutic use
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Protein-Tyrosine Kinases / antagonists & inhibitors
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Protein-Tyrosine Kinases / genetics
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Pyrimidines / therapeutic use
Substances
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Antineoplastic Agents
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Benzamides
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Piperazines
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Pyrimidines
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Imatinib Mesylate
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Interferons
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Protein-Tyrosine Kinases
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Fusion Proteins, bcr-abl