The authors report a case of simple cyst of the cerebellum documented by magnetic resonance imaging in 42-year-old men with clinical symptoms of expansive cerebellar lesion. No communication with the ventricle, no mural nodule and no enhancement after contrast injection were noted. The postoperative outcome was satisfactory after surgical removal. Histological examination of the cyst wall showed normal cerebellar tissue without epithelial lining neither tumoral features. A brief review of the seventeen cases founded in the literature is given.