Keratin-9 gene mutation in a family with epidermolytic palmoplantar keratoderma

J Eur Acad Dermatol Venereol. 2002 Mar;16(2):134-6. doi: 10.1046/j.1468-3083.2002.00426.x.

Abstract

Background: Epidermolytic palmoplantar keratoderma is an autosomal dominant inherited disorder of keratinization.

Methods: We studied five members of a Jewish family with epidermolytic palmoplantar keratoderma. Genomic DNA was extracted from leucocytes, and exon 1 of the keratin 9 gene was amplified using polymerase chain reaction techniques.

Results: The mutation was found in exon 1 of the keratin 9 gene in codon 160.

Conclusions: Like most of the other families with clinical features of epidermolytic palmoplantar keratoderma the mutation is found in exon 1 of the keratin 9 gene.

MeSH terms

  • Family
  • Female
  • Genetic Predisposition to Disease*
  • Humans
  • Israel
  • Jews / genetics*
  • Keratins / analysis
  • Keratins / genetics*
  • Keratoderma, Palmoplantar / diagnosis
  • Keratoderma, Palmoplantar / genetics*
  • Male
  • Mutation*
  • Pedigree
  • Polymerase Chain Reaction / methods

Substances

  • Keratins