[Dystrophin detection by immunofluorescent technique for diagnosing muscular dystrophy]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2002 Jun;19(3):239-42.
[Article in Chinese]

Abstract

Objective: To establish a specific technique for diagnosing and classifying Duchenne muscular dystrophy (DMD), Becker muscular dystrophy (BMD), facioscapulohumeral muscular dystrophy (FSHD) and neurologic dystrophy.

Methods: Forty-seven cases were detected by immunofluorescence technique for analyzing dystrophin located in skeletal muscle cell membrane with the use of mouse monoclonal antibodies, goat and rabbit polyclonal antibodies.

Results: The normal individuals showed ringed positive staining stripe around muscle fibers. Negative result of staining was seen in 16 DMD patients. Eleven BMD patients had discontinuous or a patchy positive staining pattern, and all of 10 FSHD and 10 neurological amyotrophic patients showed positive dystrophin staining.

Conclusion: Detecting dystrophin in the skeletal muscle cell membrane of muscular patients is an efficient technique for diagnosing and classifying various types of muscular dystrophy.

Publication types

  • English Abstract
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Child
  • Child, Preschool
  • Diagnosis, Differential
  • Dystrophin / analysis*
  • Female
  • Fluorescent Antibody Technique / methods*
  • Humans
  • Male
  • Muscle, Skeletal / chemistry
  • Muscle, Skeletal / pathology
  • Muscular Dystrophies / diagnosis*
  • Muscular Dystrophies / metabolism
  • Muscular Dystrophy, Duchenne / diagnosis
  • Muscular Dystrophy, Duchenne / metabolism
  • Muscular Dystrophy, Facioscapulohumeral / diagnosis
  • Muscular Dystrophy, Facioscapulohumeral / metabolism
  • Neuromuscular Diseases / diagnosis
  • Neuromuscular Diseases / metabolism

Substances

  • Dystrophin