Titin-cap associates with, and regulates secretion of, Myostatin

J Cell Physiol. 2002 Oct;193(1):120-31. doi: 10.1002/jcp.10158.

Abstract

Myostatin, a secreted growth factor, is a key negative regulator of skeletal muscle growth. To identify modifiers of Myostatin function, we screened for Myostatin interacting proteins. Using a yeast two-hybrid screen, we identified Titin-cap (T-cap) protein as interacting with Myostatin. T-cap is a sarcomeric protein that binds to the N-terminal domain of Titin and is a substrate of the titin kinase. Mammalian two-hybrid studies, in vitro binding assays and protein truncations in the yeast two-hybrid system verified the specific interaction between processed mature Myostatin and full-length T-cap. Analysis of protein-protein interaction using surface plasmon resonance (Biacore, Uppsala, Sweden) kinetics revealed a high affinity between Myostatin and T-cap with a KD of 40 nM. When T-cap was stably overexpressed in C(2)C(12) myoblasts, the rate of cell proliferation was significantly increased. Western analyses showed that production and processing of Myostatin were not altered in cells overexpressing T-cap, but an increase in the retention of mature Myostatin indicated that T-cap may block Myostatin secretion. Bioassay for Myostatin confirmed that conditioned media from myoblasts overexpressing T-cap contained lower levels of Myostatin. Given that Myostatin negatively regulates myoblast proliferation, the increase in proliferation observed in myoblasts overexpressing T-cap could thus be due to reduced Myostatin secretion. These results suggest that T-cap, by interacting with Myostatin, controls Myostatin secretion in myogenic precursor cells without affecting the processing step of precursor Myostatin.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Blotting, Western
  • CHO Cells
  • Cell Division / drug effects
  • Cell Line
  • Connectin
  • Cricetinae
  • Culture Media, Conditioned / metabolism
  • Culture Media, Conditioned / pharmacology
  • Genes, Reporter
  • Kinetics
  • Mice
  • Muscle Proteins / chemistry
  • Muscle Proteins / genetics
  • Muscle Proteins / metabolism*
  • Muscle Proteins / pharmacology
  • Muscle, Skeletal / cytology
  • Muscle, Skeletal / drug effects
  • Muscle, Skeletal / metabolism*
  • Myostatin
  • Protein Binding / physiology
  • Saccharomyces cerevisiae
  • Sequence Deletion
  • Surface Plasmon Resonance
  • Transfection
  • Transforming Growth Factor beta / chemistry
  • Transforming Growth Factor beta / genetics
  • Transforming Growth Factor beta / metabolism*
  • Two-Hybrid System Techniques

Substances

  • Connectin
  • Culture Media, Conditioned
  • Mstn protein, mouse
  • Muscle Proteins
  • Myostatin
  • Tcap protein, mouse
  • Transforming Growth Factor beta