Successful hematopoietic stem cell transplantation for aplastic anemia following living-related liver transplantation

Bone Marrow Transplant. 2002 Oct;30(8):531-4. doi: 10.1038/sj.bmt.1703689.

Abstract

A 1-year-old boy received a living-related liver transplantation (LRLT) from his HLA-haploidentical father to treat acute liver failure following non-A, non-B, non-C hepatitis. He subsequently developed pancytopenia and was diagnosed with aplastic anemia (AA). He was platelet transfusion dependent and developed two episodes of life-threatening intracranial hemorrhage despite immuno-suppressive therapy consisting of cyclosporin A, antithymocyte globulin, and anabolic steroids. He received combined hematopoietic stem cell transplantation (hSCT) with cord blood and bone marrow from an HLA-matched sibling. Conditioning consisted of cyclophosphamide (CY) 200 mg/kg and 7 Gy total lymphoid irradiation (TLI). Marrow engraftment was prompt and there was no significant graft-versus-host disease (GVHD).

Publication types

  • Case Reports
  • Review

MeSH terms

  • Anemia, Aplastic / etiology
  • Anemia, Aplastic / therapy*
  • Bone Marrow Transplantation
  • Cord Blood Stem Cell Transplantation
  • Disease-Free Survival
  • Hematopoietic Stem Cell Transplantation*
  • Hepatitis / complications
  • Humans
  • Infant
  • Liver Failure, Acute / complications
  • Liver Failure, Acute / therapy
  • Liver Transplantation / adverse effects*
  • Living Donors
  • Male
  • Nuclear Family
  • Remission Induction / methods