Dysregulated TCL1 promotes multiple classes of mature B cell lymphoma

Proc Natl Acad Sci U S A. 2002 Oct 29;99(22):14392-7. doi: 10.1073/pnas.212410199. Epub 2002 Oct 14.

Abstract

The TCL1 protooncogene is overexpressed in many mature B cell lymphomas, especially from AIDS patients. To determine whether aberrant expression promotes B cell transformation, we generated a murine model in which a TCL1 transgene was overexpressed at similar levels in both B and T cells. Strikingly, transgenic mice developed Burkitt-like lymphoma (BLL) and diffuse large B cell lymphoma (DLBCL) with attendant Bcl-6 expression and mutated J(H) gene segments at a very high penetrance beginning at 4 months of age. In contrast, only one mouse developed a T cell malignancy at 15 months, consistent with a longer latency for transformation of T cells by TCL1. Activation of premalignant splenic B cells by means of B cell antigen receptor (BCR) engagement resulted in significantly increased proliferation and augmented AKT-dependent signaling, including increased S6 ribosomal protein phosphorylation. Transgenic spleen cells also survived longer than wild-type spleen cells in long-term culture. Together these data demonstrate that TCL1 is a powerful oncogene that, when overexpressed in both B and T cells, predominantly yields mature B cell lymphomas.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Apoptosis
  • B-Lymphocytes / cytology
  • B-Lymphocytes / metabolism
  • Burkitt Lymphoma / metabolism*
  • Cell Division
  • Female
  • Gene Expression
  • Lymphocytosis / metabolism
  • Lymphoma, Large B-Cell, Diffuse / metabolism*
  • Lymphoproliferative Disorders / metabolism
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Transgenic
  • Protein Serine-Threonine Kinases*
  • Proto-Oncogene Proteins / genetics
  • Proto-Oncogene Proteins / metabolism*
  • Proto-Oncogene Proteins c-akt
  • Ribosomal Protein S6 / metabolism
  • Spleen / cytology
  • T-Lymphocytes / metabolism
  • Time Factors
  • Transformation, Genetic

Substances

  • Proto-Oncogene Proteins
  • Ribosomal Protein S6
  • Tcl1 protein, mouse
  • Protein Serine-Threonine Kinases
  • Proto-Oncogene Proteins c-akt