[Cholangiocarcinoma developing in von Meyenburg complexes in haemochromatosis]

Gastroenterol Clin Biol. 2002 Oct;26(10):922-4.
[Article in French]

Abstract

A 63-year-old man with genetic haemochromatosis underwent resection of a cholangiocarcinoma that developed in von Meyenburg complexes; the liver was not cirrhotic. Patients with an association of genetic haemochromatosis and von Meyenburg complexes might have a predisposition to cholangiocarcinoma, even before cirrhosis occurs. Patients with this association should undergo regular and early hepatic surveillance of hemochromatosis.

Publication types

  • Case Reports
  • English Abstract
  • Review

MeSH terms

  • Bile Duct Diseases / complications*
  • Bile Duct Diseases / pathology
  • Bile Duct Neoplasms / etiology*
  • Bile Duct Neoplasms / pathology
  • Bile Ducts, Intrahepatic / pathology
  • Cholangiocarcinoma / etiology*
  • Cholangiocarcinoma / pathology
  • Hamartoma / complications*
  • Hamartoma / pathology
  • Hemochromatosis / complications*
  • Hemochromatosis / genetics
  • Hemochromatosis / pathology
  • Humans
  • Male
  • Middle Aged
  • Risk Factors