[Allogeneic bone marrow transplantation for the treatment of Bruton disease]

Zhonghua Xue Ye Xue Za Zhi. 2002 Oct;23(10):528-30.
[Article in Chinese]

Abstract

Objective: To explore the efficacy of allogeneic bone marrow transplantation (allo-BMT) for the treatment of Bruton disease.

Methods: HLA-matched sibling bone marrow transplantation was performed for the treatment of 2 cases of X-linked agammaglobulinemia. One of them received allo-BMT twice.

Results: Recovery of hematopoiesis was gained at day 20 and day 13 after allo-BMT in the two cases respectively. Serum immunoglobin rose gradually to normal level in three months. Their humoral immuno-system was reconstituted and life quality improved. These two patients are still in disease-free survival for 13 and 2 years respectively. There was no serious graft-versus-host-disease.

Conclusion: Stem cell transplantation is a choice for the treatment of Bruton disease.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Agammaglobulinemia / blood
  • Agammaglobulinemia / therapy*
  • Bone Marrow Transplantation*
  • Child
  • Child, Preschool
  • Hemoglobins / metabolism
  • Humans
  • Immunoglobulins / blood
  • Leukocyte Count
  • Male
  • Transplantation, Homologous
  • Treatment Outcome

Substances

  • Hemoglobins
  • Immunoglobulins