E2A-PBX1 fusion in adult acute lymphoblastic leukaemia: biological and clinical features

Br J Haematol. 2003 Feb;120(3):484-7. doi: 10.1046/j.1365-2141.2003.04113.x.

Abstract

Molecular and cytogenetic studies performed in 305 adult acute lymphoblastic leukaemia (ALL) patients enrolled in the gimema (Gruppo Italiano Malattie EMatologiche dell'Adulto) multicentric protocols identified an E2A-PBX1 fusion and/or t(1;19) in 10 patients (3.3%). All had common ALL, were mostly CyIg+ and were CD34/CD13/CD33-. Nine patients achieved a complete remission (CR); five patients showed a haematological relapse after 7 months (median). Four patients are alive in first CR with a median follow-up of 29 months; three patients are molecularly negative. This abnormality is frequently associated with early treatment failure. E2A-PBX1+ adult ALL should be considered for intensified treatment strategies and monitoring of minimal residual disease.

Publication types

  • Multicenter Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Chromosomes, Human, Pair 1 / genetics
  • Chromosomes, Human, Pair 19 / genetics
  • Female
  • Follow-Up Studies
  • Homeodomain Proteins / genetics*
  • Humans
  • Karyotyping
  • Male
  • Middle Aged
  • Oncogene Proteins, Fusion / genetics*
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / drug therapy
  • Precursor Cell Lymphoblastic Leukemia-Lymphoma / genetics*
  • Prognosis
  • Recurrence
  • Translocation, Genetic
  • Treatment Failure

Substances

  • Homeodomain Proteins
  • Oncogene Proteins, Fusion
  • E2A-Pbx1 fusion protein