Neuromelanin associated redox-active iron is increased in the substantia nigra of patients with Parkinson's disease

J Neurochem. 2003 Sep;86(5):1142-8. doi: 10.1046/j.1471-4159.2003.01923.x.

Abstract

Degeneration of dopaminergic neurones during Parkinson's disease is most extensive in the subpopulation of melanized-neurones located in the substantia nigra pars compacta. Neuromelanin is a dark pigment produced in the dopaminergic neurones of the human substantia nigra and has the ability to bind a variety of metal ions, especially iron. Post-mortem analyses of the human brain have established that oxidative stress and iron content are enhanced in association with neuronal death. As redox-active iron (free Fe2+ form) and other transition metals have the ability to generate highly reactive hydroxyl radicals by a catalytic process, we investigated the redox activity of neuromelanin (NM)-aggregates in a group of parkinsonian patients, who presented a statistically significant reduction (- 70%) in the number of melanized-neurones and an increased non-heme (Fe3+) iron content as compared with a group of matched-control subjects. The level of redox activity detected in neuromelanin-aggregates was significantly increased (+ 69%) in parkinsonian patients and was highest in patients with the most severe neuronal loss. This change was not observed in tissue in the immediate vicinity of melanized-neurones. A possible consequence of an overloading of neuromelanin with redox-active elements is an increased contribution to oxidative stress and intraneuronal damage in patients with Parkinson's disease.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aged
  • Aged, 80 and over
  • Female
  • Ferric Compounds / analysis
  • Humans
  • Iron / analysis
  • Iron / metabolism*
  • Macromolecular Substances
  • Male
  • Melanins / metabolism*
  • Oxidation-Reduction
  • Parkinson Disease / pathology*
  • Prussian Blue Reaction
  • Substantia Nigra / metabolism*
  • Substantia Nigra / pathology*

Substances

  • Ferric Compounds
  • Macromolecular Substances
  • Melanins
  • neuromelanin
  • Iron