Sarcomatoid carcinoma is a high-grade neoplasm of the bladder which has a transitional, squamous or undifferentiated malign epitelial component and having areas with a sarcoma-like appearence. Most patients with sarcomatoid carcinoma are elderly males. The death rate is about 50% in these cases. Urethelial and renal pelvis involvement may occur. Metastases develop in regional lymph nodes and distant organs. In this case report, a patient who is diagnosed to have sarcomatoid carcinoma of bladder with human chorionic gonadotropin positivity, is presented and the literature is reviewed.