Acquired amegakaryocytic thrombocytopenia purpura and eosinophilic fasciitis: a long relapsing and remitting course

Am J Hematol. 2004 Mar;75(3):146-50. doi: 10.1002/ajh.10475.

Abstract

Acquired amegakaryocytic thrombocytopenia purpura (AATP) is a rare disorder of unclear etiology characterized by severe thrombocytopenia, preservation of erythroid and myeloid cell lines, and absence of megakaryocytes in the bone marrow. We report herein a patient who developed eosinophilic fasciitis preceding a diagnosis of AATP. Longitudinal follow-up and treatment of this individual show a relapsing and remitting disease course which appears closely related to the dosing of cyclosporine. Later in the treatment course, dosing of anti-thymocyte globulin (ATG) appeared to have important beneficial contributions in the management of this patient's disease.

Publication types

  • Case Reports

MeSH terms

  • Antilymphocyte Serum / therapeutic use
  • Bone Marrow / pathology
  • Cyclosporine / therapeutic use
  • Eosinophilia / blood
  • Eosinophilia / drug therapy
  • Eosinophilia / pathology*
  • Fasciitis / blood
  • Fasciitis / drug therapy
  • Fasciitis / pathology*
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Male
  • Megakaryocytes / pathology*
  • Middle Aged
  • Platelet Count
  • Purpura, Thrombocytopenic / blood
  • Purpura, Thrombocytopenic / drug therapy
  • Purpura, Thrombocytopenic / pathology*
  • Recurrence

Substances

  • Antilymphocyte Serum
  • Immunosuppressive Agents
  • Cyclosporine