Outcome for children with group III rhabdomyosarcoma treated with or without radiotherapy

Int J Radiat Oncol Biol Phys. 2004 Mar 15;58(4):1208-14. doi: 10.1016/j.ijrobp.2003.08.027.

Abstract

Purpose: To analyze the sites of relapse, relapse-free survival, and overall survival in children with Group III rhabdomyosarcoma treated with or without radiotherapy (RT).

Methods and materials: The outcomes of 48 children with Group III rhabdomyosarcoma treated between 1980 and 1997 were evaluated. The median overall survival follow-up was 7.3 years. Of the 48 patients, 65% had embryonal histology. Local treatment after induction chemotherapy included complete surgical resection (CSR) alone in 9 (19%), CSR plus RT in 13 (27%), partial resection or rebiopsy plus RT in 10 (21%), and RT alone in 15 patients (31%). One child developed distant disease before completing local therapy.

Results: Of the 48 patients, 12 developed relapse at local (n = 3), regional (n = 4), or distant (n = 5) sites. All 9 patients treated with CSR after induction chemotherapy had embryonal/botryoid histology. Only 1 of these 9 patients developed relapse. No statistically significant difference was found in overall survival (p = 0.95) or relapse-free survival (p = 0.67) between patients treated with or without RT. The Kaplan-Meier estimate of 5-year overall survival and relapse-free survival was 76% +/- 7% and 74% +/- 7%, respectively. Significant predictors of relapse-free survival on univariate analysis included CSR (p = 0.03), nodal positivity (p = 0.001), and embryonal histology (p = 0.0003). On multivariate analysis, embryonal histology was the most significant predictor of relapse-free (p = 0.001) and overall (p = 0.01) survival.

Conclusion: The overall survival for children with Group III rhabdomyosarcoma in this series was favorable. Embryonal/botryoid histology was the most significant predictor of both overall and relapse-free survival. We found that for a selected subgroup of children with embryonal histology, induction chemotherapy followed by complete surgical resection alone may be adequate local therapy.

MeSH terms

  • Adolescent
  • Analysis of Variance
  • Antineoplastic Agents / therapeutic use
  • Child
  • Child, Preschool
  • Combined Modality Therapy
  • Cyclophosphamide / therapeutic use
  • Dactinomycin / analogs & derivatives*
  • Dactinomycin / therapeutic use
  • Disease-Free Survival
  • Doxorubicin / therapeutic use
  • Epidemiologic Methods
  • Female
  • Humans
  • Infant
  • Male
  • Neoplasm Recurrence, Local
  • Radiotherapy Dosage
  • Remission Induction
  • Rhabdomyosarcoma / mortality*
  • Rhabdomyosarcoma / radiotherapy
  • Rhabdomyosarcoma / therapy*
  • Treatment Failure
  • Treatment Outcome
  • Vincristine / therapeutic use

Substances

  • Antineoplastic Agents
  • cactinomycin
  • Dactinomycin
  • Vincristine
  • Doxorubicin
  • Cyclophosphamide