Neutrophilic panniculitis with myelodysplastic syndromes presenting as pustulosis: case report and review of the literature

Am J Hematol. 2004 May;76(1):61-5. doi: 10.1002/ajh.20053.

Abstract

Neutrophilic panniculitis associated with myelodysplastic syndromes is rare. We report a 59-year-old patient who initially was diagnosed with myelodysplastic syndrome (MDS) and developed a sudden onset of widespread pustulosis and erythematous indurated papules. Examination of skin biopsies of a papule lesion showed dense neutrophilic infiltration limited to the subcutaneous tissue. The pustules and papules disappeared completely after treatment with systemic corticosteroids. To our knowledge, only one patient was identified by MEDLINE search of the English-language literature.

Publication types

  • Case Reports

MeSH terms

  • Diagnosis, Differential
  • Female
  • Humans
  • Male
  • Middle Aged
  • Myelodysplastic Syndromes / complications
  • Myelodysplastic Syndromes / diagnosis*
  • Panniculitis / complications
  • Panniculitis / diagnosis*
  • Panniculitis / drug therapy
  • Skin Diseases, Vesiculobullous / diagnosis*
  • Steroids / therapeutic use
  • Sweet Syndrome / complications
  • Sweet Syndrome / diagnosis*
  • Sweet Syndrome / drug therapy

Substances

  • Steroids