Aim: To evaluate the frequency of the co-occurrence of a retinoma and another primary tumor.
Method: Presentation of a case report and review of the literature.
Results: A cutaneous melanoma was observed in a 52-year-old man, who was known to have two retinomas in the right eye. Five other cases were found in a review of the literature, suggesting the possibility of an increased risk of developing a second primary tumor in patients with retinoma. The occurrence of cutaneous melanoma as a second primary tumor after retinoma and/or retinoblastoma is discussed.
Conclusion: There might be an increased risk for patients with retinoma to develop another primary tumor, necessitating regular follow-up of these patients.