Regression of severe pulmonary arteriovenous malformations after Fontan revision and "hepatic factor" rerouting

Nancy A Pike; Luca A Vricella; Jeffrey A Feinstein; Michael D Black; Bruce A Reitz

doi:10.1016/j.athoracsur.2004.02.003

Regression of severe pulmonary arteriovenous malformations after Fontan revision and "hepatic factor" rerouting

Ann Thorac Surg. 2004 Aug;78(2):697-9. doi: 10.1016/j.athoracsur.2004.02.003.

Authors

Nancy A Pike¹, Luca A Vricella, Jeffrey A Feinstein, Michael D Black, Bruce A Reitz

Affiliation

¹ Division of Cardiothoracic Surgery, David Geffen School of Medicine at University of California-Los Angeles, UCLA Box 951741, Los Angeles, CA 90095-1741, USA. [email protected]

PMID: 15276554
DOI: 10.1016/j.athoracsur.2004.02.003

Abstract

Although previously described in patients undergoing staged palliation for univentricular heart disease, the mechanism by which hepatic venous flow prevents development of pulmonary arteriovenous malformations is still not completely understood. We present a case in which successful H-type Fontan revision with rerouting of hepatic venous flow through a hemiazygous vein successfully reversed the progression of severe left pulmonary arteriovenous malformations.

Publication types

Case Reports

MeSH terms

Abnormalities, Multiple / surgery*
Arteriovenous Fistula / etiology
Arteriovenous Fistula / surgery*
Arteriovenous Shunt, Surgical
Child
Cyanosis
Female
Fontan Procedure*
Heart Defects, Congenital / surgery*
Heart Ventricles / abnormalities*
Hemorheology
Hepatic Veins / surgery*
Humans
Palliative Care
Postoperative Complications / etiology
Postoperative Complications / surgery*
Prostheses and Implants
Pulmonary Artery / surgery*
Pulmonary Valve / surgery
Situs Inversus
Venae Cavae / abnormalities