Recurrent fatal pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance

Francesca Santamaria; Gianluca Brancaccio; Giancarlo Parenti; Paola Francalanci; Cosimo Squitieri; Gianfranco Sebastio; Carlo Dionisi-Vici; Patrizia D'argenio; Generoso Andria; Francesco Parisi

doi:10.1016/j.jpeds.2004.04.047

Recurrent fatal pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance

J Pediatr. 2004 Aug;145(2):268-72. doi: 10.1016/j.jpeds.2004.04.047.

Authors

Francesca Santamaria¹, Gianluca Brancaccio, Giancarlo Parenti, Paola Francalanci, Cosimo Squitieri, Gianfranco Sebastio, Carlo Dionisi-Vici, Patrizia D'argenio, Generoso Andria, Francesco Parisi

Affiliation

¹ Department of Pediatrics, Federico II University, Naples, Italy.

PMID: 15289783
DOI: 10.1016/j.jpeds.2004.04.047

Abstract

We present a case of recurrent pulmonary alveolar proteinosis after heart-lung transplantation in a child with lysinuric protein intolerance. The recurrence of the pulmonary disease provides further insight regarding the possible pathogenesis of pulmonary alveolar proteinosis and therapeutic options for this complication.

Publication types

Case Reports

MeSH terms

Amino Acid Transport Disorders, Inborn / complications*
Amino Acid Transport Disorders, Inborn / urine
Fatal Outcome
Heart-Lung Transplantation*
Humans
Infant
Lysine / urine
Male
Pulmonary Alveolar Proteinosis / complications*
Pulmonary Alveolar Proteinosis / surgery*
Recurrence

Substances

Lysine