Monocytosis and accelerated activation of lymphocytes in C1q-deficient autoimmune-prone mice

Immunology. 2004 Sep;113(1):80-8. doi: 10.1111/j.1365-2567.2004.01940.x.

Abstract

C1q deficiency has been shown to accelerate spontaneous autoimmunity in mice. We studied the time course of activation of monocytes and lymphocytes in autoimmune and non-autoimmune mice in the presence or absence of C1q as a disease accelerator. Autoimmune MRL\Mp.C1qa-\- and non-autoimmune C57BL\6.C1qa-\- mice were analysed at various time points between 6 and 33 weeks of age and compared to strain- and age-matched C1q-sufficient controls. Splenic and peritoneal leucocytes were analysed by flow cytometry and plasma levels of immunoglobulin M (IgM), total IgG, IgG subclasses and IgM autoantibodies were measured. Both C1q-deficient strains had significantly more splenic monocytes than their controls at all time points analysed. In addition, MRL\Mp.C1qa-\- but not C57BL/6.C1qa-\- mice developed splenic hypercellularity starting at about 12-17 weeks old, had signs of accelerated CD4+ T-cell activation and showed a marked increase in splenic plasma cells and total serum IgM levels from about 22 weeks of age. The accelerated CD4+ T-cell activation was not due to a direct inhibitory effect of C1q on T cells. These data show that C1q deficiency causes splenic monocytosis together with accelerated T-cell activation in an autoimmune-prone mouse strain.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Autoimmune Diseases / immunology*
  • B-Lymphocytes / immunology
  • CD4-Positive T-Lymphocytes / immunology
  • Cell Division / immunology
  • Cells, Cultured
  • Complement C1q / deficiency*
  • Female
  • Genetic Predisposition to Disease*
  • Immunoglobulin M / blood
  • Immunophenotyping
  • Lupus Erythematosus, Systemic / immunology
  • Lymphocyte Activation / immunology*
  • Mice
  • Mice, Inbred C57BL
  • Monocytes / immunology*
  • Spleen / immunology

Substances

  • Immunoglobulin M
  • Complement C1q