G6PD/PK ratio: a reliable parameter to identify glucose-6-phosphate dehydrogenase deficiency associated with microcytic anemia in heterozygous subjects

Clin Biochem. 2004 Oct;37(10):863-6. doi: 10.1016/j.clinbiochem.2004.06.011.

Abstract

Objectives: To determine if measuring the ratio of glucose-6-phosphate dehydrogenase (G6PD) to pyruvate kinase (PK) is more reliable than only measuring G6PD activity to identify heterozygous G6PD- individuals with associated microcytic anemia in the Calabrian population, which shows high frequencies of both the thalassaemia (thal) trait and G6PD deficiency.

Design and methods: Measurement of G6PD and PK activities was carried out on 205 samples of whole blood from Calabrian subjects of both sexes (age range 10-50 years) using a double starter differential pH-metry technique.

Results: The G6PD/PK ratio is able to differentiate G6PD- heterozygous individuals from the normal population. G6PD/PK values also allowed us to easily identify the G6PD- heterozygous subjects with microcytic anaemia. Student's t test shows that G6PD/PK ratio is more reliable in both sample groups, relative to G6PD activity in normal subjects.

Conclusions: G6PD/PK ratio is a reliable diagnostic parameter for mass screening for G6PD deficiency.

MeSH terms

  • Adolescent
  • Adult
  • Anemia / complications
  • Anemia / diagnosis*
  • Anemia / enzymology
  • Biomarkers / blood*
  • Child
  • Female
  • Glucosephosphate Dehydrogenase / blood*
  • Glucosephosphate Dehydrogenase Deficiency / complications
  • Glucosephosphate Dehydrogenase Deficiency / diagnosis*
  • Glucosephosphate Dehydrogenase Deficiency / enzymology
  • Heterozygote
  • Humans
  • Male
  • Mass Screening
  • Middle Aged
  • Pyruvate Kinase / blood*
  • Thalassemia / complications
  • Thalassemia / diagnosis
  • Thalassemia / enzymology

Substances

  • Biomarkers
  • Glucosephosphate Dehydrogenase
  • Pyruvate Kinase