Granzyme B induces smooth muscle cell apoptosis in the absence of perforin: involvement of extracellular matrix degradation

Arterioscler Thromb Vasc Biol. 2004 Dec;24(12):2245-50. doi: 10.1161/01.ATV.0000147162.51930.b7. Epub 2004 Oct 7.

Abstract

Objective: T cell-induced cytotoxicity, of which granzyme B is a key mediator, is believed to contribute to the pathogenesis of inflammatory vascular diseases. In this report, we investigate the mechanism of granzyme B-induced smooth muscle cell (SMC) death.

Methods and results: The addition of purified granzyme B alone to cultured SMCs caused a significant reduction in cell viability. Chromatin condensation, phosphatidylserine externalization, and membrane blebbing were observed, indicating that the mechanism of granzyme B-induced SMC death was through apoptosis. Activated splenocytes from perforin-knockout mice induced SMC death through a granzyme B-mediated pathway. Inhibition of the proteolytic activities of caspases and granzyme B prevented granzyme B-induced SMC death, whereas attenuation of granzyme B internalization with mannose-6-phosphate (M6P) did not. Further, granzyme B induced the cleavage of several SMC extracellular proteins, including fibronectin, and reduced focal adhesion kinase phosphorylation.

Conclusions: These results indicate that granzyme B can induce apoptosis of SMCs in the absence of perforin by cleaving extracellular proteins, such as fibronectin.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Apoptosis / physiology*
  • Caspase 3
  • Caspases / metabolism
  • Cell Line, Tumor
  • Cell Survival / physiology
  • Coronary Vessels / enzymology
  • Coronary Vessels / metabolism
  • Extracellular Matrix / enzymology
  • Extracellular Matrix / metabolism*
  • Extracellular Matrix Proteins / metabolism
  • Granzymes
  • HeLa Cells / chemistry
  • HeLa Cells / metabolism
  • Humans
  • Membrane Glycoproteins / deficiency*
  • Membrane Glycoproteins / physiology
  • Mice
  • Mice, Inbred C57BL
  • Muscle, Smooth, Vascular / enzymology
  • Muscle, Smooth, Vascular / physiology
  • Myocytes, Smooth Muscle / enzymology
  • Myocytes, Smooth Muscle / physiology*
  • Perforin
  • Pore Forming Cytotoxic Proteins
  • Rats
  • Serine Endopeptidases / metabolism
  • Serine Endopeptidases / physiology*
  • Spleen / cytology
  • Spleen / metabolism

Substances

  • Extracellular Matrix Proteins
  • Membrane Glycoproteins
  • Pore Forming Cytotoxic Proteins
  • Perforin
  • GZMB protein, human
  • Granzymes
  • Gzmb protein, mouse
  • Gzmb protein, rat
  • Serine Endopeptidases
  • CASP3 protein, human
  • Casp3 protein, mouse
  • Casp3 protein, rat
  • Caspase 3
  • Caspases