High telomerase activity in granulocytes from clonal polycythemia vera and essential thrombocythemia

Blood. 2005 Mar 1;105(5):2138-40. doi: 10.1182/blood-2004-06-2375. Epub 2004 Oct 19.

Abstract

Essential thrombocythemia (ET) and polycythemia vera (PV) are chronic myeloproliferative disorders that share the involvement of a multipotent progenitor cell and dominance of the transformed clone over normal hematopoiesis. On the other hand, the heterogeneity of these diseases with respect to clonal development from a common progenitor has been well established. To identify useful prognostic indicators, we analyzed telomerase activity (TA), a known marker of neoplastic proliferation, in granulocytes (PMNs) and mononuclear cells (MNCs) from 22 female patients with ET and PV. Clonality status was determined by investigation of X chromosome inactivation patterns (XCIPs). We found a statistically significant positive correlation between high TA and monoclonal pattern of XCIP. Therefore, our data suggest that the use of multiple tumor markers may contribute to a better understanding of the deregulated physiology of these disorders and provide useful prognostic factors.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Biomarkers, Tumor / analysis
  • Clone Cells
  • Dosage Compensation, Genetic
  • Female
  • Granulocytes / metabolism
  • Granulocytes / pathology*
  • Humans
  • Leukocytes, Mononuclear / metabolism
  • Middle Aged
  • Polycythemia Vera / genetics
  • Polycythemia Vera / pathology*
  • Prognosis
  • Telomerase / metabolism*
  • Thrombocythemia, Essential / genetics
  • Thrombocythemia, Essential / pathology*

Substances

  • Biomarkers, Tumor
  • Telomerase