ZAP-70 directly enhances IgM signaling in chronic lymphocytic leukemia

Blood. 2005 Mar 1;105(5):2036-41. doi: 10.1182/blood-2004-05-1715. Epub 2004 Oct 28.

Abstract

Chronic lymphocytic leukemia (CLL) B cells that express unmutated immunoglobulin heavy-chain variable region genes (IgV(H)) generally express ZAP-70, in contrast to normal B cells or most CLL cases with mutated IgV(H). Following IgM ligation, ZAP-70+ CLL cells had significantly higher levels of phosphorylated p72(Syk), BLNK, and phospholipase-Cgamma (PLCgamma) and had greater[Ca2+]i flux than did ZAP-70-negative CLL cases, including unusual ZAP-70-negative cases with unmutated IgV(H). IgM ligation of ZAP-70-negative CLL B cells infected with an adenovirus vector encoding ZAP-70 induced significantly greater levels of phosphorylated p72(Syk), BLNK, and PLCgamma and had greater[Ca2+]i flux than did similarly stimulated, noninfected CLL cells or CLL cells infected with a control adenovirus vector. We conclude that expression of ZAP-70 in CLL allows for more effective IgM signaling in CLL B cells, a feature that could contribute to the relatively aggressive clinical behavior generally associated with CLL cells that express unmutated IgV(H).

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adaptor Proteins, Signal Transducing
  • B-Lymphocytes / immunology
  • B-Lymphocytes / pathology
  • Carrier Proteins / metabolism
  • Enzyme Precursors / metabolism
  • Humans
  • Immunoglobulin Heavy Chains
  • Immunoglobulin M / physiology*
  • Immunoglobulin Variable Region
  • Intracellular Signaling Peptides and Proteins
  • Leukemia, Lymphocytic, Chronic, B-Cell / immunology*
  • Phospholipase C gamma
  • Phosphoproteins / metabolism
  • Phosphorylation
  • Protein-Tyrosine Kinases / metabolism
  • Protein-Tyrosine Kinases / physiology*
  • Signal Transduction*
  • Syk Kinase
  • Type C Phospholipases / metabolism
  • ZAP-70 Protein-Tyrosine Kinase

Substances

  • Adaptor Proteins, Signal Transducing
  • B cell linker protein
  • Carrier Proteins
  • Enzyme Precursors
  • Immunoglobulin Heavy Chains
  • Immunoglobulin M
  • Immunoglobulin Variable Region
  • Intracellular Signaling Peptides and Proteins
  • Phosphoproteins
  • Protein-Tyrosine Kinases
  • SYK protein, human
  • Syk Kinase
  • ZAP-70 Protein-Tyrosine Kinase
  • ZAP70 protein, human
  • Type C Phospholipases
  • Phospholipase C gamma