Emergent bullectomy for acute respiratory failure in Ehlers-Danlos syndrome

Zeenat Safdar; Mary O'Sullivan; Janet M Shapiro

doi:10.1177/0885066604269645

Emergent bullectomy for acute respiratory failure in Ehlers-Danlos syndrome

J Intensive Care Med. 2004 Nov-Dec;19(6):349-51. doi: 10.1177/0885066604269645.

Authors

Zeenat Safdar¹, Mary O'Sullivan, Janet M Shapiro

Affiliation

¹ Division of Pulmonary-Critical Care Medicine, Columbia University of Physicians & Surgeons, St. Luke's-Roosevelt Hospital Center, 432 W. 58th Street, Rm 520, New York, NY 10019, USA. [email protected].

PMID: 15523121
DOI: 10.1177/0885066604269645

Abstract

A 49-year-old man with Ehlers-Danlos syndrome developed acute respiratory failure requiring mechanical ventilation. Chest computed tomography demonstrated giant right bulla extending into the contralateral hemithorax with mediastinal shift. Surgical bullectomy with pleurodesis relieved tension effects and allowed weaning.

Publication types

Case Reports

MeSH terms

Acute Disease
Adult
Biopsy
Cough / etiology
Critical Care / methods
Dyspnea / etiology
Ehlers-Danlos Syndrome / complications*
Emergencies
Fever / etiology
Humans
Male
Pneumonectomy
Positive-Pressure Respiration / adverse effects
Pulmonary Emphysema / diagnosis
Pulmonary Emphysema / etiology*
Pulmonary Emphysema / surgery*
Respiratory Insufficiency / diagnosis
Respiratory Insufficiency / etiology*
Respiratory Insufficiency / surgery*
Risk Factors
Smoking / adverse effects
Tomography, X-Ray Computed
Treatment Outcome