Enhanced arteriogenesis and wound repair in dystrophin-deficient mdx mice

Circulation. 2004 Nov 23;110(21):3341-8. doi: 10.1161/01.CIR.0000147776.50787.74. Epub 2004 Nov 15.

Abstract

Background: The absence of functional dystrophin in Duchenne muscular dystrophy (DMD) patients and in mdx mice results in progressive muscle degeneration associated with necrosis, fibrosis, and inflammation. Because vascular supply plays a key role in tissue repair, we examined whether new blood vessel development was altered in mdx mice.

Methods and results: In a model of hindlimb ischemia on femoral artery dissection, hindlimb perfusion, measured by laser Doppler imaging, was higher in mdx mice (0.67+/-0.26) than in wild-type (WT) mice (0.33+/-0.18, P<0.03). In keeping with these data, a significant increase in arteriole length density was found in mdx mice (13.6+/-8.4 mm/mm3) compared with WT mice (7.8+/-4.6 mm/mm3, P<0.03). Conversely, no difference was observed in capillary density between mice of the 2 genotypes. The enhanced regenerative response was not limited to ischemic skeletal muscle, because in a wound-healing assay, mdx mice showed an accelerated wound closure rate compared with WT mice. Moreover, a vascularization assay in Matrigel plugs containing basic fibroblast growth factor injected subcutaneously revealed an increased length density of arterioles in mdx (46.9+/-14.7 mm/mm3) versus WT mice (19.5+/-5.8 mm/mm3, P<0.001). Finally, serum derived from mdx mice sustained formation of endothelium-derived tubular structures in vitro more efficiently than WT serum.

Conclusions: These results demonstrate that arteriogenesis is enhanced in mdx mice both after ischemia and skin wounding and in response to growth factors.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Arterioles / ultrastructure
  • Capillaries / ultrastructure
  • Collagen
  • Colony-Forming Units Assay
  • Drug Combinations
  • Dystrophin / physiology*
  • Femoral Artery / injuries
  • Fibroblast Growth Factor 2 / administration & dosage
  • Fibroblast Growth Factor 2 / pharmacology
  • Hematopoietic Stem Cell Mobilization
  • Hindlimb / blood supply*
  • Ischemia / physiopathology*
  • Laminin
  • Male
  • Mice
  • Mice, Inbred C57BL
  • Mice, Inbred mdx
  • Muscle, Skeletal / physiology*
  • Neovascularization, Physiologic / physiology*
  • Proteoglycans
  • Regeneration
  • Wound Healing / physiology*

Substances

  • Drug Combinations
  • Dystrophin
  • Laminin
  • Proteoglycans
  • Fibroblast Growth Factor 2
  • matrigel
  • Collagen