Familial ptotic lid elevation during ipsilateral abduction

J AAPOS. 2004 Dec;8(6):571-5. doi: 10.1016/j.jaapos.2004.07.010.

Abstract

Purpose: To report and discuss the clinical findings of a 17-member family with 2 siblings who exhibit ptosis and abnormal synkinetic lid elevation associated with ipsilateral abduction.

Subjects and methods: Sixteen members of the 17-member immediate family underwent ophthalmic examination.

Results: Two siblings exhibited ptosis and abnormal synkinetic lid elevation associated with ipsilateral abduction. One was bilaterally affected and the other had unilateral findings. A third sibling had isolated bilateral congenital ptosis. A fourth demonstrated classic Duane syndrome Type I in the right eye. Other family members did not have ophthalmic abnormalities.

Conclusions: A unifying mechanism of congenital cranial dysinnervation may underlie these and similar phenotypes of oculomotor and/or abducens nerve abnormalities with or without abnormal synkinesis.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Blepharoptosis / genetics*
  • Child, Preschool
  • Eyelids / innervation*
  • Female
  • Humans
  • Male
  • Ocular Motility Disorders / genetics*
  • Ocular Motility Disorders / physiopathology
  • Oculomotor Muscles / innervation*
  • Oculomotor Nerve / abnormalities*
  • Pedigree