Background: Congenital choledochal cyst is a rare kind of bile duct deformity, resulting from cystic or shuttle-like dilation of part of the choledochal duct congenitally. We present a 20-year-old girl with a congenital choledochal cyst complicated by acute pancreatitis.
Method: The clinical data of the woman with a congenital choledochal cyst concurrent with acute pancreatitis were retrospectively analyzed.
Result: The congenital choledochal cyst of the woman was type IV complicated by acute pancreatitis.
Conclusions: The diagnosis of congenital choledochal cyst mainly depends on CT, MRCP, and ERCP. Total excision of the choledochal cyst with Roux-en-Y hepaticojejunostomy is recommended as the treatment. For patients with type V cysts with frequently recurrent cholangitis resulting biliary liver cirrhosis, liver transplantation should be considered.