Severe left ventricular dysfunction secondary to primary pulmonary hypertension: bridging therapy with bosentan before lung transplantation

J Heart Lung Transplant. 2005 Jun;24(6):777-80. doi: 10.1016/j.healun.2004.02.020.

Abstract

When right ventricular failure develops secondary to primary pulmonary hypertension, right-left ventricular interaction may lead to severe impairment of left ventricular function. In such cases, many experts favor combined heart-lung transplantation by fear that the left ventricle may not recover after transplantation of the lungs alone. We report a case of primary pulmonary hypertension with severely diminished right and left ventricular function. The patient was rendered amenable to isolated pulmonary transplantation with the endothelin-receptor antagonist bosentan. The medication improved right and left ventricular function to the point that heart transplantation no longer appeared necessary. After double-lung transplantation the patient's cardiac function made a full recovery. This approach might be particularly welcome considering both the current donor organ shortage and the limited number of surgical teams with expertise in heart-lung transplantation.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Antihypertensive Agents / therapeutic use*
  • Bosentan
  • Combined Modality Therapy
  • Humans
  • Hypertension, Pulmonary / complications
  • Hypertension, Pulmonary / therapy*
  • Lung Transplantation*
  • Male
  • Severity of Illness Index
  • Sulfonamides / therapeutic use*
  • Ventricular Dysfunction, Left / etiology*
  • Ventricular Dysfunction, Right / etiology*

Substances

  • Antihypertensive Agents
  • Sulfonamides
  • Bosentan