Dual targeting of transformed and untransformed HTLV-1-infected T cells by DHMEQ, a potent and selective inhibitor of NF-kappaB, as a strategy for chemoprevention and therapy of adult T-cell leukemia

Blood. 2005 Oct 1;106(7):2462-71. doi: 10.1182/blood-2004-09-3646. Epub 2005 Jun 14.

Abstract

Human T-cell leukemia virus type I (HTLV-1) causes adult T-cell leukemia (ATL), a fatal T-cell leukemia resistant to chemotherapy, after more than 50 years of clinical latency from transmission through breast-feeding. Polyclonal expansion of virus-infected T cells predisposes them to transformation. Constitutive activation of nuclear factor-kappaB (NF-kappaB) in the leukemic cells is essential for their growth and survival. Blocking NF-kappaB has been shown to be a potential strategy to treat ATL. We tested this approach using a novel NF-kappaB inhibitor, dehydroxymethylepoxyquinomicin (DHMEQ), and also examined its application to chemoprevention by selective purging of the HTLV-1-infected cells. DHMEQ inhibited NF-kappaB activation in primary ATL cells and cell lines derived from them and induced apoptotic cell death. NF-kappaB inhibition down-regulated expression of genes involved in antiapoptosis or cell-cycle progression. DHMEQ protected severe combined immunodeficiency (SCID) mice inoculated with HTLV-1-transformed cells from death. In addition, DHMEQ selectively targeted HTLV-1-infected cells in the peripheral blood of virus carriers in vitro, resulting in a decreased number of infected cells. We conclude that NF-kappaB is a potential molecular target for treatment and prevention of ATL. As a potent NF-kappaB inhibitor, DHMEQ is a promising compound allowing the translation of this strategy into clinical medicine.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Antineoplastic Agents / pharmacology*
  • Apoptosis
  • Benzamides / pharmacology*
  • Caspases / metabolism
  • Cell Cycle
  • Cell Line
  • Cell Line, Transformed
  • Cell Line, Tumor
  • Cell Proliferation
  • Cyclohexanones / pharmacology*
  • Dose-Response Relationship, Drug
  • Down-Regulation
  • Gene Expression Regulation, Neoplastic*
  • Genes, Reporter
  • Human T-lymphotropic virus 1 / metabolism*
  • Humans
  • Immunoblotting
  • Immunohistochemistry
  • Jurkat Cells
  • K562 Cells
  • Leukemia, T-Cell / drug therapy*
  • Leukemia, T-Cell / prevention & control*
  • Leukemia, T-Cell / virology
  • Leukemia-Lymphoma, Adult T-Cell / drug therapy*
  • Leukemia-Lymphoma, Adult T-Cell / virology
  • Leukocytes, Mononuclear / cytology
  • Leukocytes, Mononuclear / metabolism
  • Male
  • Mice
  • Mice, SCID
  • Microscopy, Fluorescence
  • Molecular Weight
  • NF-kappa B / antagonists & inhibitors*
  • NF-kappa B / metabolism
  • Proviruses
  • Reverse Transcriptase Polymerase Chain Reaction
  • T-Lymphocytes / virology*
  • Time Factors
  • Tumor Suppressor Protein p53 / metabolism

Substances

  • Antineoplastic Agents
  • Benzamides
  • Cyclohexanones
  • NF-kappa B
  • Tumor Suppressor Protein p53
  • dehydroxymethylepoxyquinomicin
  • Caspases