[Multicentric reticulohistiocytosis: report of a case with systemic disease]

Ann Pathol. 2005 Feb;25(1):50-3. doi: 10.1016/s0242-6498(05)80099-9.
[Article in French]

Abstract

Multicentric reticulohistiocytosis (RHM) is a rare non Langherhans cell histiocytosis with skin and joint involvment. Nearly all organs can be involved. Association with cancer occurs in about 25% of cases. Association with auto-immune diseases has also been recorded. Microscopic examination shows a histiocytic nodular infiltrate made of giant cells with ground-glass appearance and PAS positive cytoplasm. Immunostaining shows cell positivity for CD68 and negativity for CD1a and S100 protein. No Birbeck granules are found at ultrastructural examination.

Publication types

  • Case Reports
  • English Abstract

MeSH terms

  • Adult
  • Antigens, CD / analysis
  • Antigens, Differentiation, Myelomonocytic / analysis
  • Biopsy
  • Bone Marrow / pathology
  • Cytoplasm / pathology
  • Female
  • Histiocytes / pathology
  • Histiocytosis, Non-Langerhans-Cell / diagnosis*
  • Histiocytosis, Non-Langerhans-Cell / pathology
  • Humans
  • Immunohistochemistry
  • Immunophenotyping
  • Microscopy, Electron
  • Muscles / pathology
  • Periodic Acid-Schiff Reaction
  • Skin / pathology

Substances

  • Antigens, CD
  • Antigens, Differentiation, Myelomonocytic
  • CD68 antigen, human