Incidence, clinical outcome, and management of virus-induced hemorrhagic cystitis in children and adolescents after allogeneic hematopoietic cell transplantation

Biol Blood Marrow Transplant. 2005 Oct;11(10):797-804. doi: 10.1016/j.bbmt.2005.06.007.

Abstract

We analyzed the incidence, etiology, risk factors, and clinical management of hemorrhagic cystitis (HC) in 102 children who underwent allogeneic stem cell transplantation: 28 from matched siblings, 57 from unrelated donors, and 17 from mismatched relatives. Conditioning regimens consisted of high-dose chemotherapy (n=83) or total body irradiation (n=19). In all children, urine and plasma were prospectively screened for human polyomavirus (HPV; BK virus [BKV] and JC virus [JCV]) or adenovirus (AdV) DNA with a polymerase chain reaction-based assay. Viral DNA was detected in the urine of 56 children (54.9%): BKV in 48 (47%), JCV in 4 (3.9%), and AdV in 4 (3.9%). HC occurred in 26 children (25.5%), and viruria was detected in all of them: BKV in 21 (80.8%), AdV in 4 (14.4%), and JCV in 1 (3.8%). All patients with AdV viruria developed HC. The cumulative incidence of HC in patients with HPV viruria was 0.43. The only significant risk factor for HC in patients with HPV-positive urine was conditioning with high-dose chemotherapy. Twenty-two children were treated with cidofovir, with no significant toxicity. In all treated patients but 1, the clinical symptoms were moderate, and no HC-related death was observed. We conclude that virus-induced HC is a frequent complication after allogeneic hematopoietic cell transplantation. Treatment with cidofovir is feasible, and further studies are warranted to evaluate its activity in HC mediated by BKV or JCV.

MeSH terms

  • Adenoviridae / isolation & purification
  • Adolescent
  • Adult
  • Child
  • Child, Preschool
  • Cidofovir
  • Cystitis / drug therapy
  • Cystitis / epidemiology
  • Cystitis / etiology
  • Cystitis / virology*
  • Cytosine / analogs & derivatives
  • Cytosine / therapeutic use
  • DNA, Viral / blood
  • DNA, Viral / urine
  • Disease Management
  • Female
  • Hematopoietic Stem Cell Transplantation / adverse effects*
  • Hematopoietic Stem Cell Transplantation / methods
  • Hemorrhage
  • Humans
  • Incidence
  • Infant
  • JC Virus / isolation & purification
  • Male
  • Mass Screening
  • Organophosphonates / therapeutic use
  • Polyomavirus / isolation & purification
  • Prospective Studies
  • Risk Factors
  • Transplantation Conditioning / adverse effects
  • Transplantation Conditioning / methods
  • Transplantation, Homologous
  • Treatment Outcome
  • Viruses / isolation & purification*

Substances

  • DNA, Viral
  • Organophosphonates
  • Cytosine
  • Cidofovir