Arrhythmogenic cardiomyopathy of the right ventricle is characterized by replacement of right myocardial cells by fibro-fatty tissue and arrhythmias. The authors present two cases where EKG gated multislice CT was valuable. In one case, comprehensive evaluation of extensive ventricular dysplasia complicated by intraventricular thrombus was achieved whereas accurate evaluation of the ventricular wall process was possible in another case.