Abstract
A case of neonatal epileptic encephalopathy with suppression-bursts associated with olivary dentate nuclei dysplasia is reported. This unusual association shows that the so-called Ohtahara syndrome could correspond to several different brain malformations sometimes disclosable only by neuropathological examination.
MeSH terms
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Cerebellar Nuclei / pathology
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Cerebellar Nuclei / physiopathology*
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Dominance, Cerebral / physiology
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Electroencephalography*
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Evoked Potentials / physiology
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Female
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Humans
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Infant
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Olivary Nucleus / pathology
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Olivary Nucleus / physiopathology*
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Spasms, Infantile / pathology
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Spasms, Infantile / physiopathology*