Primary cilia of inv/inv mouse renal epithelial cells sense physiological fluid flow: bending of primary cilia and Ca2+ influx

Cell Struct Funct. 2005;30(2):93-100. doi: 10.1247/csf.30.93.

Abstract

Primary cilia are hypothesized to act as a mechanical sensor to detect renal tubular fluid flow. Anomalous structure of primary cilia and/or impairment of increases in intracellular Ca2+ concentration in response to fluid flow are thought to result in renal cyst formation in conditional kif3a knockout, Tg737 and pkd1/pkd2 mutant mice. The mutant inv/inv mouse develops multiple renal cysts like kif3a, Tg737 and pkd1/pkd2 mutants. Inv proteins have been shown to be localized in the renal primary cilia, but response of inv/inv cilia to fluid stress has not been examined. In the present study, we examined the mechanical response of primary cilia to physiological fluid flow using a video microscope, as well as intracellular Ca2+ increases in renal epithelial cells from normal and inv/inv mice in response to flow stress. Percentages of ciliated cells and the length of primary cilia were not significantly different between primary renal cell cultures from normal and inv/inv mutant mice. Localization of inv protein was restricted to the base of primary cilia even under flow stress. Inv/inv mutant cells had similar bending mechanics of primary cilia in response to physiological fluid flow compared to normal cells. Furthermore, no difference was found in intracellular Ca2+ increases in response to physiological fluid flow between normal and inv/inv mutant cells. Our present study suggests that the function of the inv protein is distinct from polaris (the Tg737 gene product), polycystins (pkd1 and pkd2 gene products).

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Calcium / metabolism*
  • Cells, Cultured
  • Cilia / chemistry
  • Cilia / physiology*
  • Cilia / ultrastructure
  • Epithelial Cells / chemistry
  • Epithelial Cells / physiology*
  • Epithelial Cells / ultrastructure
  • Extracellular Fluid / metabolism*
  • Kidney / chemistry
  • Kidney / cytology
  • Kidney / physiology*
  • Kidney / ultrastructure
  • Kidney Diseases, Cystic / metabolism
  • Kidney Diseases, Cystic / physiopathology
  • Membrane Proteins / genetics
  • Membrane Proteins / physiology
  • Mice
  • Mice, Mutant Strains
  • Mice, Transgenic
  • Microscopy, Video
  • Proteins / genetics
  • Proteins / physiology
  • TRPP Cation Channels
  • Transcription Factors / analysis
  • Transcription Factors / genetics
  • Transcription Factors / physiology
  • Tumor Suppressor Proteins / genetics
  • Tumor Suppressor Proteins / physiology

Substances

  • Invs protein, mouse
  • Membrane Proteins
  • Proteins
  • TRPP Cation Channels
  • Tg737Rpw protein, mouse
  • Transcription Factors
  • Tumor Suppressor Proteins
  • polycystic kidney disease 1 protein
  • polycystic kidney disease 2 protein
  • Calcium