Congenital gliosarcoma; so-called sarcoglioma

Childs Nerv Syst. 1990 Nov;6(7):416-20. doi: 10.1007/BF00302231.

Abstract

A mixed glioma and sarcoma in a 3-month-old infant is presented as a rare case of gliosarcoma with a good response to treatment. This congenital case is quite different from those in adults: the tumor cells were mainly composed of sarcomatous elements; glial components were not anaplastic without obvious endothelial hyperplasia, but presented as reticulin-free islands, mimicking a reactive glioma in a sarcoma. It may be termed "sarcoglioma" to distinguish from a classic gliosarcoma. The origin of the rare mixed tumor may be related to a dysgenesis of both mesenchymal and glial elements.

Publication types

  • Case Reports

MeSH terms

  • Basal Ganglia / pathology
  • Basal Ganglia Diseases / pathology
  • Basal Ganglia Diseases / surgery*
  • Brain Neoplasms / congenital*
  • Brain Neoplasms / pathology
  • Brain Neoplasms / radiotherapy
  • Brain Neoplasms / surgery
  • Combined Modality Therapy
  • Cranial Irradiation
  • Female
  • Follow-Up Studies
  • Glial Fibrillary Acidic Protein / analysis
  • Gliosarcoma / congenital*
  • Gliosarcoma / pathology
  • Gliosarcoma / radiotherapy
  • Gliosarcoma / surgery
  • Humans
  • Immunoenzyme Techniques
  • Infant
  • Microscopy, Electron
  • Parietal Lobe / pathology
  • Parietal Lobe / surgery*
  • Temporal Lobe / pathology
  • Temporal Lobe / surgery*

Substances

  • Glial Fibrillary Acidic Protein