Hepatocellular carcinoma in Wilson's disease: a rare association in childhood

Pediatr Transplant. 2006 Aug;10(5):639-43. doi: 10.1111/j.1399-3046.2006.00562.x.

Abstract

Wilson's disease is a hereditary disorder of copper metabolism that results in the accumulation of copper in the body, primarily in the liver, brain, and cornea. Hepatocellular carcinoma, in contrast to other causes of cirrhosis, is seldom associated with Wilson's disease. We present a 12-yr-old boy with Wilson's disease in whom hepatocellular carcinoma was incidentally diagnosed in the pathologic specimen examined after liver transplantation.

Publication types

  • Case Reports

MeSH terms

  • Carcinoma, Hepatocellular / etiology*
  • Child
  • Hepatolenticular Degeneration / complications*
  • Hepatolenticular Degeneration / surgery*
  • Humans
  • Incidental Findings
  • Liver Neoplasms / etiology*
  • Liver Transplantation*
  • Male