Expression of non-signaling membrane-anchored death receptors protects murine livers in different models of hepatitis

Hepatology. 2006 Aug;44(2):399-409. doi: 10.1002/hep.21257.

Abstract

Fas and tumor necrosis factor receptor 1 (TNFR1) are death receptors involved in various diseases such as hepatitis, sepsis, or graft rejection. Neutralizing antibodies to death ligands or soluble death receptors can inhibit cell death; however, they induce side effects because of their systemic actions. To specifically block death signaling to target cells, we created death domain-deficient (DeltaDD) membrane-anchored receptors, delivered to the liver by either recombinant adenovirus or hydrodynamic pressure of nonviral recombinant plasmids. In anti-Fas antibody-induced fulminant hepatitis, mice expressing recombinant Fas-decoy receptors (FasDeltaDD) in their livers were completely protected against apoptosis and survived fulminant hepatitis. In T-cell-dependent concanavalin A-induced autoimmune hepatitis, FasDeltaDD antagonist expression prevented hepatocyte damage and mouse death. Finally, TNFR1DeltaDD effectively protected mice against LPS-induced septic shock. In conclusion, such DeltaDD-decoy receptors act as dominant-negative receptors exerting local inhibition, while avoiding systemic neutralization of apoptosis ligands, and might have therapeutic potential in hepatitis.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Signal Transducing / biosynthesis
  • Adaptor Proteins, Signal Transducing / genetics*
  • Animals
  • Apoptosis / physiology*
  • Blotting, Western
  • Disease Models, Animal
  • Fas-Associated Death Domain Protein
  • Female
  • Gene Expression*
  • Hepatitis / metabolism*
  • Hepatitis / pathology
  • Hepatitis / prevention & control
  • Membrane Glycoproteins / metabolism
  • Mice
  • Mice, Inbred BALB C
  • RNA / genetics*
  • Reverse Transcriptase Polymerase Chain Reaction

Substances

  • Adaptor Proteins, Signal Transducing
  • Fadd protein, mouse
  • Fas-Associated Death Domain Protein
  • Membrane Glycoproteins
  • RNA