Malpuech syndrome: broadening the clinical spectrum and molecular analysis by array-CGH

Eur J Med Genet. 2007 Mar-Apr;50(2):139-43. doi: 10.1016/j.ejmg.2006.10.004. Epub 2006 Oct 28.

Abstract

We report on a patient with mental and growth retardation, bilateral cleft lip and palate, hypertelorism, ptosis, hearing loss and mild epispadias, suggestive of Malpuech syndrome. High-resolution karyotype and microarray-CGH using an oligonucleotide array with 75Kb oligo's were normal, excluding Wolf-Hirschhorn syndrome. Long-term follow-up revealed psychiatric manifestations starting at young age.

Publication types

  • Case Reports
  • Comparative Study

MeSH terms

  • Abnormalities, Multiple / genetics*
  • Abnormalities, Multiple / pathology
  • Adolescent
  • Cleft Lip / genetics
  • Cleft Lip / pathology
  • Cleft Palate / genetics
  • Cleft Palate / pathology
  • DNA / genetics
  • Dwarfism / genetics*
  • Dwarfism / pathology
  • Follow-Up Studies
  • Humans
  • Hypertelorism / genetics
  • Hypertelorism / pathology
  • Intellectual Disability / genetics*
  • Intellectual Disability / pathology
  • Male
  • Nucleic Acid Hybridization / methods*
  • Oligonucleotide Array Sequence Analysis / methods*
  • Syndrome
  • Time Factors

Substances

  • DNA