Lupus-related advanced liver involvement as the initial presentation of systemic lupus erythematosus

J Microbiol Immunol Infect. 2006 Dec;39(6):471-5.

Abstract

Background and purpose: Systemic lupus erythematosus (SLE), a prototype of systemic autoimmune disease characterized by multiorgan involvement with diverse clinical and serological manifestations, principally affects women in their child-bearing years. Clinically significant hepatic abnormality as the initial presentation of SLE has rarely been reported.

Methods: Eleven patients with lupus with initial presentation of lupus-related hepatitis were included in this retrospective review. Clinical manifestation, immunological profiles, and risk factors for poor prognosis were analyzed.

Results: The most commonly associated clinical manifestations were found to be thrombocytopenia, leukopenia, advancing age, and presence of anti-SSA/Ro antibody and anti-thyroid antibodies. The diagnosis of SLE was delayed due to dominant hepatic abnormalities. Age greater than 50 years and marked hepatic decompensation in accordance with Child classification B and C might suggest poor prognosis (p=0.06). However, the p value was not statistically significant because of the small sample size.

Conclusions: Lupus-related hepatitis, particularly in late-onset lupus, is common. In addition, the presence of anti-SSA, anti-thyroglobulin, and anti-microsomal antibodies is indicative of hepatic involvement in patients with SLE.

MeSH terms

  • Adult
  • Aged
  • Aging
  • Antibodies / blood
  • Autoantibodies
  • Autoantigens / immunology
  • Female
  • Hepatitis / complications*
  • Hepatitis / physiopathology
  • Humans
  • Leukopenia / pathology
  • Lupus Erythematosus, Systemic / diagnosis
  • Lupus Erythematosus, Systemic / etiology*
  • Lupus Vulgaris / complications*
  • Male
  • Middle Aged
  • RNA, Small Cytoplasmic / immunology
  • Retrospective Studies
  • Ribonucleoproteins / immunology
  • Thrombocytopenia / pathology
  • Thyroid Gland / immunology

Substances

  • Antibodies
  • Autoantibodies
  • Autoantigens
  • RNA, Small Cytoplasmic
  • RO60 protein, human
  • Ribonucleoproteins
  • anti-thyroglobulin