Aim: To describe a malignant cystic nephroma in an asymptomatic man.
Methods: Case report and review of the literature.
Results: A 60 year old white male presented with an incidentally discovered right perirenal mass. An MRI demonstrated a large perinephric encapsulated mass with diffuse heterogeneity. Patient underwent a radical nephrectomy and retroperitoneal node dissection. Histopathological analyses of the resected specimen revealed malignant cystic nephroma.
Conclusion: This represents the first published report of this rare tumor in an adult patient.