Perivascular epithelioid cell tumor (PEComa) in the genitourinary tract

Adv Anat Pathol. 2007 Jan;14(1):36-41. doi: 10.1097/PAP.0b013e31802e0dc4.

Abstract

Perivascular epithelioid cell tumors (PEComas) are mesenchymal tumors composed of histologically, immunohistochemically, ultrastructurally, and genetically distinctive cells. PEComas have been described in different organs and are considered ubiquitous tumors. In this review we discuss recent informations related to PEComas in the genitourinary tract.

Publication types

  • Review

MeSH terms

  • Angiomyolipoma / genetics
  • Angiomyolipoma / metabolism
  • Angiomyolipoma / pathology
  • Biomarkers, Tumor / metabolism
  • Epithelioid Cells / metabolism
  • Epithelioid Cells / pathology*
  • Female
  • Gene Deletion
  • Humans
  • Male
  • Neoplasms, Connective and Soft Tissue / genetics
  • Neoplasms, Connective and Soft Tissue / metabolism
  • Neoplasms, Connective and Soft Tissue / pathology*
  • Tuberous Sclerosis / pathology
  • Urogenital Neoplasms / genetics
  • Urogenital Neoplasms / metabolism
  • Urogenital Neoplasms / pathology*

Substances

  • Biomarkers, Tumor