A structural core within apolipoprotein C-II amyloid fibrils identified using hydrogen exchange and proteolysis

J Mol Biol. 2007 Mar 9;366(5):1639-51. doi: 10.1016/j.jmb.2006.12.040. Epub 2006 Dec 21.

Abstract

Plasma apolipoproteins show alpha-helical structure in the lipid-bound state and limited conformational stability in the absence of lipid. This structural instability of lipid-free apolipoproteins may account for the high propensity of apolipoproteins to aggregate and accumulate in disease-related amyloid deposits. Here, we explore the properties of amyloid fibrils formed by apolipoproteins using human apolipoprotein (apo) C-II as a model system. Hydrogen-deuterium exchange and NMR spectroscopy of apoC-II fibrils revealed core regions between residues 19-37 and 57-74 with reduced amide proton exchange rates compared to monomeric apoC-II. The C-terminal core region was also identified by partial proteolysis of apoC-II amyloid fibrils using endoproteinase GluC and proteinase K. Complete tryptic hydrolysis of apoC-II fibrils followed by centrifugation yielded a single peptide in the pellet fraction identified using mass spectrometry as apoC-II(56-76). Synthetic apoC-II(56-76) readily formed fibrils, albeit with a different morphology and thioflavinT fluorescence yield compared to full-length apoC-II. Studies with smaller peptides narrowed this fibril-forming core to a region within residues 60-70. We postulate that the ability of apoC-II(60-70) to independently form amyloid fibrils drives fibril formation by apoC-II. These specific amyloid-forming regions within apolipoproteins may underlie the propensity of apolipoproteins and their peptide derivatives to accumulate in amyloid deposits in vivo.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Motifs
  • Amino Acid Sequence
  • Amyloid / chemistry*
  • Amyloid / ultrastructure
  • Apolipoprotein C-II / chemistry*
  • Apolipoprotein C-II / isolation & purification
  • Apolipoprotein C-II / ultrastructure
  • Benzothiazoles
  • Chromatography, High Pressure Liquid
  • Circular Dichroism
  • Deuterium / metabolism*
  • Deuterium Exchange Measurement
  • Dose-Response Relationship, Drug
  • Electrophoresis, Agar Gel
  • Endopeptidase K / pharmacology
  • Fluorescent Dyes
  • Humans
  • Hydrogen / metabolism*
  • Hydrolysis
  • Kinetics
  • Mass Spectrometry
  • Molecular Sequence Data
  • Nuclear Magnetic Resonance, Biomolecular
  • Protein Conformation
  • Protein Folding
  • Protein Structure, Tertiary
  • Serine Endopeptidases / pharmacology
  • Spectrometry, Fluorescence
  • Thiazoles
  • Time Factors
  • Trypsin / pharmacology

Substances

  • Amyloid
  • Apolipoprotein C-II
  • Benzothiazoles
  • Fluorescent Dyes
  • Thiazoles
  • apolipoprotein C-II (St Michael)
  • thioflavin T
  • Hydrogen
  • Deuterium
  • Serine Endopeptidases
  • glutamyl endopeptidase
  • Trypsin
  • Endopeptidase K