Orofacial dystonia related to Sjogren's syndrome

Sokratis G Papageorgiou; Theodoros Kontaxis; Anastasios Bonakis; Nikolaos Kalfakis

doi:10.1007/s10067-006-0519-4

Orofacial dystonia related to Sjogren's syndrome

Clin Rheumatol. 2007 Oct;26(10):1779-81. doi: 10.1007/s10067-006-0519-4. Epub 2007 Jan 16.

Authors

Sokratis G Papageorgiou¹, Theodoros Kontaxis, Anastasios Bonakis, Nikolaos Kalfakis

Affiliation

¹ Department of Neurology, Eginition Hospital, Medical School, University of Athens, 74, Vassilissis Sofias Avenue, 11528 Athens, Greece. [email protected]

PMID: 17225057
DOI: 10.1007/s10067-006-0519-4

Abstract

Sjogren's syndrome (SS), either primary or secondary, is rarely accompanied by CNS complications. We report the exceptional case of a patient with secondary SS, who presented orofacial dystonia as a consequence of her disease. Initial treatment with clonazepam and levetiracetam was unsuccessful. However, dystonia was dramatically improved by a treatment with corticosteroids. This case demonstrates that corticosteroids can be efficacious in the treatment of dystonia related to SS.

Publication types

Case Reports

MeSH terms

Adrenal Cortex Hormones / therapeutic use
Brain / pathology
Clonazepam / therapeutic use
Dystonia
Dystonic Disorders / complications*
Dystonic Disorders / diagnosis
Face / pathology*
Female
Humans
Levetiracetam
Magnetic Resonance Imaging / methods
Middle Aged
Piracetam / analogs & derivatives
Piracetam / therapeutic use
Remission Induction
Sjogren's Syndrome / complications*
Sjogren's Syndrome / diagnosis
Treatment Outcome

Substances

Adrenal Cortex Hormones
Levetiracetam
Clonazepam
Piracetam