Congenital abnormal synkinesis involving the eyelid, which is well described in the Marcus Gunn jaw-winking phenomenon, also has been reported in association with axons intended for facial musculature, extraocular muscles, and the pupil.(1,2) The subject of this report is a novel form in which the patient's ptotic eyelid elevated only during contralateral head tilt when the patient was upright, suggesting a congenital abnormality within the otolith-oculomotor pathway.