Cellular oligomerization of alpha-synuclein is determined by the interaction of oxidized catechols with a C-terminal sequence

J Biol Chem. 2007 Oct 26;282(43):31621-30. doi: 10.1074/jbc.M704737200. Epub 2007 Sep 4.

Abstract

The mechanisms that govern the formation of alpha-synuclein (alpha-syn) aggregates are not well understood but are considered a central event in the pathogenesis of Parkinson's disease (PD). A critically important modulator of alpha-syn aggregation in vitro is dopamine and other catechols, which can prevent the formation of alpha-syn aggregates in cell-free and cellular model systems. Despite the profound importance of this interaction for the pathogenesis of PD, the processes by which catechols alter alpha-syn aggregation are unclear. Molecular and biochemical approaches were employed to evaluate the mechanism of catechol-alpha-syn interactions and the effect on inclusion formation. The data show that the intracellular inhibition of alpha-syn aggregation requires the oxidation of catechols and the specific noncovalent interaction of the oxidized catechols with residues (125)YEMPS(129) in the C-terminal region of the protein. Cell-free studies using novel near infrared fluorescence methodology for the detection of covalent protein-ortho-quinone adducts showed that although covalent modification of alpha-syn occurs, this does not affect alpha-syn fibril formation. In addition, oxidized catechols are unable to prevent both thermal and acid-induced protein aggregation as well as fibrils formed from a protein that lacks a YEMPS amino acid sequence, suggesting a specific effect for alpha-syn. These results suggest that inappropriate C-terminal cleavage of alpha-syn, which is known to occur in vivo in PD brain or a decline of intracellular catechol levels might affect disease progression, resulting in accelerated alpha-syn inclusion formation and dopaminergic neurodegeneration.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Amino Acid Sequence
  • Catechols / metabolism*
  • Cell Line, Tumor
  • Cell-Free System
  • Fluorescent Antibody Technique, Indirect
  • Formazans / metabolism
  • Genetic Vectors
  • Humans
  • Lentivirus / genetics
  • Light
  • Mass Spectrometry
  • Neuroblastoma / pathology
  • Oxidation-Reduction
  • Plasmids
  • Recombinant Proteins / isolation & purification
  • Recombinant Proteins / metabolism
  • Scattering, Radiation
  • Spectrometry, Fluorescence
  • Transduction, Genetic
  • Transfection
  • alpha-Synuclein / chemistry*
  • alpha-Synuclein / genetics
  • alpha-Synuclein / metabolism*

Substances

  • Catechols
  • Formazans
  • Recombinant Proteins
  • alpha-Synuclein
  • nitroblue formazan