Abstract
The development of Philadelphia chromosome-positive chronic myelogenous leukemia (CML) in the adolescent population is very rare. CML occurring as a secondary malignancy in individuals treated for anaplastic large cell lymphoma (ALCL) is also rare. We present the case of a 16-year-old adolescent boy who developed a right orbital mass that was diagnosed as ALCL with the t(2;5)(p23;q25) chromosomal aberration. Four years after receiving treatment for ALCL, he presented with a swollen leg and a white cell count of 431,000. Peripheral blood and bone marrow evaluation revealed a myeloproliferative disorder. Cytogenetic and molecular studies demonstrated the presence of t(9;22). We present the histopathologic, molecular, and cytogenetic findings of this patient's initial presentation with systemic ALCL as well as his secondary presentation with CML 4 years later. Therapy-related CML and non-therapy-related secondary CML are discussed as potential explanations of this highly unusual clinical presentation.
MeSH terms
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Adolescent
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Anaplastic Lymphoma Kinase
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Antineoplastic Combined Chemotherapy Protocols / therapeutic use
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Bone Marrow Transplantation
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Cyclophosphamide / therapeutic use
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Daunorubicin / therapeutic use
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Flow Cytometry
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Fusion Proteins, bcr-abl / genetics
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Humans
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In Situ Hybridization, Fluorescence
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Leukemia, Myelogenous, Chronic, BCR-ABL Positive / genetics
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Leukemia, Myelogenous, Chronic, BCR-ABL Positive / pathology*
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Leukemia, Myelogenous, Chronic, BCR-ABL Positive / therapy
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Lymphoma, Large B-Cell, Diffuse / drug therapy
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Lymphoma, Large B-Cell, Diffuse / metabolism
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Lymphoma, Large B-Cell, Diffuse / pathology*
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Male
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Neoplasms, Second Primary / genetics
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Neoplasms, Second Primary / pathology*
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Neoplasms, Second Primary / therapy
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Orbital Neoplasms / pathology
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Protein-Tyrosine Kinases / metabolism*
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Receptor Protein-Tyrosine Kinases
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Reverse Transcriptase Polymerase Chain Reaction
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Vincristine / therapeutic use
Substances
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Vincristine
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Cyclophosphamide
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ALK protein, human
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Anaplastic Lymphoma Kinase
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Protein-Tyrosine Kinases
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Receptor Protein-Tyrosine Kinases
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Fusion Proteins, bcr-abl
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Daunorubicin