Abstract
Pulmonary arterial hypertension represents an absolute contraindication for heart transplantation. We report the case of a 30-year-old man with end-stage heart failure due to restrictive cardiomyopathy and pulmonary arterial hypertension. A complex multidrug therapy improved pulmonary haemodynamics to the point that orthotopic heart transplantation could be carried out. At 18-month follow-up after heart transplantation, the patient's cardiac function made a full recovery. Larger prospective studies are warranted to support these results.
MeSH terms
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Adult
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Antihypertensive Agents / administration & dosage*
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Bosentan
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Cardiac Catheterization
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Cardiomyopathy, Restrictive / complications
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Cardiomyopathy, Restrictive / physiopathology
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Contraindications
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Drug Therapy, Combination
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Epoprostenol / administration & dosage*
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Heart Failure / etiology
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Heart Failure / physiopathology
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Heart Failure / surgery*
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Heart Transplantation*
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Humans
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Hypertension, Pulmonary / complications
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Hypertension, Pulmonary / drug therapy*
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Hypertension, Pulmonary / physiopathology
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Male
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Sulfonamides / administration & dosage*
Substances
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Antihypertensive Agents
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Sulfonamides
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Epoprostenol
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Bosentan