Growth of children with hypochondroplasia treated with growth hormone for up to three years

Horm Res. 1991:36 Suppl 1:56-60. doi: 10.1159/000182190.

Abstract

Hypochondroplasia is a skeletal dysplasia characterised by poor childhood growth and an inadequate pubertal growth spurt. 31 children with a radiological diagnosis of hypochondroplasia have been treated for up to 3 years with recombinant human growth hormone, mean dose 17.9 U/m2/week as daily subcutaneous injections. Mean pre-treatment height velocity standard deviation score (SDS) was -0.51; this increased to +1.58 after 1 year of treatment. This improvement diminishes over the next 2 years. The effect on final height remains unknown. There was a considerable variation in clinical response within the group treated.

MeSH terms

  • Adolescent
  • Body Height*
  • Bone Diseases, Developmental / drug therapy*
  • Bone Diseases, Developmental / physiopathology
  • Child
  • Child, Preschool
  • Growth Hormone / therapeutic use*
  • Humans
  • Recombinant Proteins / therapeutic use

Substances

  • Recombinant Proteins
  • Growth Hormone