[Diabetic ketoacidosis with a fatal issue: is it a MODY3 (maturity-onset diabetes of the young type 3)?]

Ann Biol Clin (Paris). 2008 Mar-Apr;66(2):189-93. doi: 10.1684/abc.2008.0201.
[Article in French]

Abstract

Ketoacidotic coma is one of the possible diabetes mellitus first symptoms. It results from complete or relative lack of insuline and is often associated with type 1 diabetes. The authors report a case of a 45-years old woman with inaugural diabetes of which atypical features have motivated the study of MODY gene (maturity-onset diabetes of the young). Gly574ser polymorphism in the HNF-1alpha gene was found, in homozygous state, and the question of the responsibility of this polymorphism in this diabete is asked.

Publication types

  • Case Reports
  • Comparative Study
  • English Abstract

MeSH terms

  • Diabetes Mellitus, Type 1 / diagnosis
  • Diabetes Mellitus, Type 1 / genetics
  • Diabetes Mellitus, Type 2 / diagnosis
  • Diabetes Mellitus, Type 2 / genetics
  • Diabetic Coma*
  • Diabetic Ketoacidosis* / diagnosis
  • Diabetic Ketoacidosis* / genetics
  • Diagnosis, Differential
  • Fatal Outcome
  • Female
  • Glycine / genetics
  • Hepatocyte Nuclear Factor 1-alpha* / genetics
  • Hepatocyte Nuclear Factor 4 / genetics
  • Humans
  • Middle Aged
  • Mutation
  • Polymorphism, Genetic
  • Prognosis

Substances

  • HNF1A protein, human
  • HNF4A protein, human
  • Hepatocyte Nuclear Factor 1-alpha
  • Hepatocyte Nuclear Factor 4
  • Glycine